Audio file

Reid Final.mp3

Transcript

00:00:00 Jenn Dawson

Hello and welcome to PeDRA Pearls, the podcast from the Pediatric Dermatology Research Alliance.

00:00:06 Jenn Dawson

We are a vibrant research community pursuing a mission to create, inspire, and sustain research to prevent, treat, and cure childhood skin disease.

00:00:16 Jenn Dawson

Each week, we bring you inspiring stories, research updates, and practical information to advance science that improves the lives of children with skin diseases and conditions.

00:00:27 Jenn Dawson

I'm Jenn Dawson, host of PeDRA Pearls and PeDRA’s Director of Educational Programs.

00:00:33 Jenn Dawson

I'm so glad you're here.

00:00:39 Jenn Dawson

In this episode, I sit down with Dr.

00:00:41 Jenn Dawson

Reid Oldenburg for an in-depth conversation about his path into dermatology, his passion for translational research, and his leadership of PeDRA’s Drugs and Bugs focused study group.

00:00:53 Jenn Dawson

Dr.

00:00:53 Jenn Dawson

Oldenburg shares how early experiences, from field research on rare infectious diseases in West Africa to complex immunology lab work, shaped his clinician-scientist career.

00:01:06 Jenn Dawson

Together, we explore the origins and purpose of the Drugs and Bugs Focus Study Group, the importance of clearly defining conditions like RIME and SJS and TEN,

00:01:18 Jenn Dawson

and the major ongoing research efforts aimed at improving diagnosis, treatment, and patient support for severe cutaneous adverse reactions.

00:01:28 Jenn Dawson

So let's jump in.

00:01:29 Jenn Dawson

Welcome to PeDRA Pearls, Dr.

00:01:31 Jenn Dawson

Oldenburg.

00:01:31 Jenn Dawson

I am so excited to be speaking with you today.

00:01:34 Jenn Dawson

So let's start with a little bit of background about you.

00:01:38 Jenn Dawson

Tell me about your journey into dermatology and research.

00:01:43 Reid Oldenburg

Yeah, thanks.

00:01:44 Reid Oldenburg

Yeah, thanks so much for having me.

00:01:45 Reid Oldenburg

It's so cool to finally be here.

00:01:47 Reid Oldenburg

And I'm so glad that I've had a chance to work on some of the projects and report back to you.

00:01:51 Reid Oldenburg

So yeah, thanks again.

00:01:53 Reid Oldenburg

I'm Reed Oldenburg.

00:01:54 Reid Oldenburg

I'm an MD-PhD, so I'm a clinician scientist.

00:01:57 Reid Oldenburg

And I work at UC San Diego, the VA, and at Rady Hospitals.

00:02:01 Reid Oldenburg

My breakdown currently is I do about 40% of my time in the clinic.

00:02:07 Reid Oldenburg

And then I've always really liked research.

00:02:09 Reid Oldenburg

So I'm spending as much time as I can in the lab and doing about 60%

00:02:13 Reid Oldenburg

percent of my time doing research.

00:02:15 Reid Oldenburg

And a lot of the research has been very translational because I've been focused just on getting high-quality patient samples, understanding the inflammation and the immunology and the immunopathomechanisms of disease in these patients.

00:02:30 Reid Oldenburg

And so yeah, I really do, I'm kind of a jack of all trades right now, but I really do, the biggest focus of my work is in the translational science

00:02:39 Reid Oldenburg

space.

00:02:40 Jenn Dawson

And was research always the career goal for you, or is that something you discovered a passion for at some point in your training?

00:02:48 Jenn Dawson

Can you talk a little bit more about that?

00:02:50 Reid Oldenburg

Yeah, I definitely always knew that I wanted to do basic science research, and I wasn't sure.

00:02:56 Reid Oldenburg

Sure, exactly.

00:02:56 Reid Oldenburg

In the beginning, if I wanted to do medicine, but once I got into research, I was working in a couple different labs as a research assistant.

00:03:03 Reid Oldenburg

And once I started to be in the lab, I realized how much I wanted to work with people and actually see patients.

00:03:10 Reid Oldenburg

And I really felt like the most interesting research really comes from things that are happening in real people because patients obviously with an inflammatory disease, there's so much to be understood about the particular patient, but then there's a huge thing that there's just so much to understand about the disease in general.

00:03:27 Reid Oldenburg

And with all of the new science that we have, we have new techniques that can understand disease processes, but then we also have new drugs that are being marketed and approved so that we can combine techniques with medications to really make

00:03:40 Reid Oldenburg

make patients' lives better.

00:03:42 Reid Oldenburg

And I think my personal journey really started with, I was doing a summer internship at the Pasteur Institute in Paris.

00:03:48 Reid Oldenburg

And I got involved in a project that to me was very translational, where we actually, I was sent in the field in West Africa and Ghana to study a rare dermatologic infectious disease called Buruli ulcer that is caused by an actual mycobacteria.

00:04:05 Reid Oldenburg

And I just felt like it was so fun to be there in person, meeting the

00:04:10 Reid Oldenburg

patients.

00:04:10 Reid Oldenburg

And it was such an understudied disease at the time that it was just, to me, it was so exciting to actually talk to patients, go visit the towns where maybe they were getting infected with the pathogen, and then actually you collect samples from the patients, get clinical data from them.

00:04:25 Reid Oldenburg

So I felt like it was a very alive research project that made me really enjoy the whole process.

00:04:31 Reid Oldenburg

And it was so social, it was so fun.

00:04:34 Reid Oldenburg

So that was really, I think, my initial introduction to translational research.

00:04:40 Reid Oldenburg

And then during that project in the lab, I was offered a PhD spot to continue research in mycobacterial infections.

00:04:48 Reid Oldenburg

So mycobacteria cause, you know, Hans' disease or formerly known as leprosy, they cause tuberculosis.

00:04:54 Reid Oldenburg

And then I ended up doing a very rigorous or more strict PhD in understanding the host pathogen interactions of how mycobacteria, how they alter immune function and how they infect people in the 1st place.

00:05:07 Reid Oldenburg

So it was like, it went from really the patient-centered thing into the lab.

00:05:11 Reid Oldenburg

So I followed that trajectory, which is pretty much how I started in the world of research.

00:05:18 Reid Oldenburg

When it comes to drugs and bugs and the work that I've been now lucky enough to have been a part

00:05:24 Reid Oldenburg

or be a part of PeDRA and work on.

00:05:26 Reid Oldenburg

When it comes to drugs and bugs, it really started once again with the patient again, where I was a dermatology resident and I started seeing patients with reactive infectious mucocutaneous eruptions or RIME.

00:05:38 Reid Oldenburg

Being an immunologist or being a sort of,

00:05:41 Reid Oldenburg

aspiring immunologist, I kept wondering, what is actually going on in these patients?

00:05:45 Reid Oldenburg

what actually causes the blistering?

00:05:47 Reid Oldenburg

And after talking with, my mentors like, Larry Eichenfield, I started to learn that there were so many more questions.

00:05:54 Reid Oldenburg

And that's how I ended up meeting folks in PeDRA and how I really found a way into my current lab and current research setup where I work.

00:06:02 Jenn Dawson

Oh my goodness.

00:06:03 Jenn Dawson

Thank you so much for sharing that background into what inspired you to be both in the lab and working with patients.

00:06:10 Jenn Dawson

This is just really cool.

00:06:12 Jenn Dawson

I had no idea about your story and your trip to Africa.

00:06:15 Jenn Dawson

That sounds amazing.

00:06:16 Jenn Dawson

So there's a lot that I want to go in on here.

00:06:19 Jenn Dawson

But let's first, let's kind of focus on the drugs and bugs piece, because you did mention drugs and bugs.

00:06:25 Jenn Dawson

And that is what we call a research focused study group here at PeDRA.

00:06:30 Jenn Dawson

For those listeners who are unfamiliar, PeDRA sort of brackets their research in these different buckets of disease focused area.

00:06:37 Jenn Dawson

So drugs and bugs is one of our newer

00:06:40 Jenn Dawson

of study groups.

00:06:42 Jenn Dawson

So if you could just give our listeners like a quick definition of what that group is.

00:06:46 Jenn Dawson

I know you mentioned rhyme, but let's kind of dive into what that group is and then we can talk about what it does.

00:06:53 Reid Oldenburg

Right, so in my understanding of the history of drugs and bugs, because it predates me, is that it really was related in the beginning to understanding some of the severe cutaneous adverse reactions and really focused on pediatric dermatology patients.

00:07:08 Reid Oldenburg

So drugs and bugs, I think, started off early with just trying to define some of the terms.

00:07:14 Reid Oldenburg

And I think the term

00:07:16 Reid Oldenburg

RIME, or Reactive Infectious Myocoputaneous Eruption, essentially was in the early stages of the FSG before it really formally existed.

00:07:25 Reid Oldenburg

And so essentially, drugs and bugs was designed to answer everything that is drugs and bugs.

00:07:31 Reid Oldenburg

So of course, the major focus would be the scary things in pediatric dermatology, which are the severe cutaneous adverse reaction.

00:07:39 Reid Oldenburg

So pediatric dermatology, you know, having fewer expert clinicians in the community and then having

00:07:46 Reid Oldenburg

less research previously in the adult world.

00:07:50 Reid Oldenburg

I think for the FSG, it was really dedicated to bringing together the brightest minds in North America and internationally and really studying everything that is drugs and bugs.

00:08:02 Reid Oldenburg

But of course, historically, it has been more focused on the pathogen-triggered mucocutaneous eruptions like Ryme and then, of course, Steven-Johnson syndrome, toxic epidermal necrolysis,

00:08:15 Reid Oldenburg

in some of these really rare and severe diseases.

00:08:18 Reid Oldenburg

But in reality, drugs and bugs would cover anything that is drugs or bugs.

00:08:23 Reid Oldenburg

So of course, there have been other projects on tinea or ringworm.

00:08:29 Reid Oldenburg

There have been projects on medications and other allergies.

00:08:32 Reid Oldenburg

So it really is a wide basket.

00:08:34 Reid Oldenburg

And now, one of the other medications that, of course, our group is now studying are JAK inhibitors and how that affects people.

00:08:41 Reid Oldenburg

So really, it's a very broad

00:08:44 Reid Oldenburg

FSG that covers a lot of different topics, but historically, and I think our current projects really are majorly focused on the severe cutaneous adverse reactions.

00:08:53 Jenn Dawson

And what was it about severe cutaneous adverse reactions that really attracted you and that you wanted to learn more about?

00:09:00 Reid Oldenburg

I think that by definition, they're severe and they're very terrible.

00:09:03 Reid Oldenburg

So I think when you're, as a dermatologist, you know, these are some of the scariest things that we see in clinic.

00:09:10 Reid Oldenburg

or in the hospital.

00:09:11 Reid Oldenburg

And these are patients that are really suffering A lot.

00:09:14 Reid Oldenburg

So I think just for immediately, of course, in training and then in the early years after training, it's a very easy thing to want to help patients with because the patients present so dramatically, they're so sick.

00:09:26 Reid Oldenburg

And then there's also so many major questions in understanding these diseases, both clinically and from a basic science perspective, that it makes it in a lot of ways, it makes it very easy to be attracted to because it's like, there's so much potential to help people essentially.

00:09:40 Jenn Dawson

Yeah, I can definitely see why you and your colleagues who are studying these severe cutaneous adverse reactions are so passionate about it.

00:09:51 Jenn Dawson

And now you are leading the charge as the chair of this group.

00:09:55 Jenn Dawson

So give me some details and some insider information into what the group is working on, what projects are upcoming, if you need any collaborators.

00:10:04 Jenn Dawson

I just want to know what's going on in the group.

00:10:07 Reid Oldenburg

Right, and there's a lot of ongoing projects and it's always a challenge because everyone has their full clinical schedule to work with.

00:10:16 Reid Oldenburg

So our projects are have a little bit of a, they have, it's like a, it's almost like a dinosaur walking, like it takes time to make progress, but we are moving.

00:10:24 Reid Oldenburg

We have momentum and everything, you know, happens in time.

00:10:29 Reid Oldenburg

And we have a lot of ongoing projects.

00:10:31 Reid Oldenburg

In terms of discussing ways to help, I'm going to share with you a,

00:10:37 Reid Oldenburg

an electronic system that we have where we can actually track different projects.

00:10:42 Reid Oldenburg

So I'll share that with you and you can put the link in the bio as well, because we're looking for ways to match people and we have chat rooms and we have ways that we can set deadlines.

00:10:51 Reid Oldenburg

So I'll definitely share that with you.

00:10:53 Reid Oldenburg

The group is, there's a major focus, of course, as in PeDRA, to really bring together the minds that we have and develop consensus, and it can be consensus via, can we come up with consensus guidelines to better treat, to diagnose?

00:11:10 Reid Oldenburg

And of course, historically, this FSG has really been dedicated to Rhyme because that's where a lot of major questions still exist.

00:11:17 Reid Oldenburg

So the group at large, the FSG, many of the individual members of our group are working on developing consensus guidelines.

00:11:25 Reid Oldenburg

So one ongoing

00:11:29 Reid Oldenburg

publication will be dedicated to just bringing clinicians together and providing a nice roadmap for those that are maybe less expert and those that are residents that are trying to learn more about rhyme and to revise the diagnostic criteria.

00:11:43 Reid Oldenburg

So there's definitely a focus to improve our

00:11:46 Reid Oldenburg

our outward communication on what rhyme is.

00:11:49 Reid Oldenburg

And then there is an ongoing consensus, really bringing the actual, the best minds of rhyme together and then identifying good treatment algorithms.

00:11:59 Reid Oldenburg

So I think that's a really nice upcoming publication that I would anticipate we would be seeing in the next one to two years.

00:12:07 Reid Oldenburg

And I think that will be really helpful because really, it's, I think it's really interesting talking to, you know, the great minds of rhyme, like, you know, Yvonne Chu and Michelle Ramin,

00:12:15 Reid Oldenburg

There are so many things that are very intuitive to them because they have a high volume of patients that they take care of.

00:12:21 Reid Oldenburg

And what we really want to do is we want to try and transmit some of these key knowledge points between the key opinion leaders and give it to the public so that the, or just residents and maybe younger faculty members, so that they can take this and understand some of these intuitive points and operationalize them and actually say, okay, how do I measure this?

00:12:41 Reid Oldenburg

How do I understand if a patient's progressing?

00:12:43 Reid Oldenburg

How do I decide to go up with therapy?

00:12:44 Reid Oldenburg

So I think those

00:12:45 Reid Oldenburg

That's going to be a major, I think, one of our capstone projects in the next one to two years that I'm very excited about.

00:12:51 Jenn Dawson

Well, those two projects in and of themselves sound like a massive undertaking and something that this space really, really needs, especially when you're talking about educating other providers who are going to be seeing this

00:13:05 Jenn Dawson

in their ERs or in their clinical practice.

00:13:07 Jenn Dawson

What else is going on in the group?

00:13:09 Reid Oldenburg

So one of the projects that we have that's ongoing, that I'm not directly involved in, that I'm very excited about, is Yvonne Chu, Michelle Romine, and Beth Rolle.

00:13:18 Reid Oldenburg

I think it was back in 2020, they launched a project

00:13:21 Reid Oldenburg

to study Ryme patients and then do genetic sequencing of them and their parents.

00:13:27 Reid Oldenburg

So the idea here is really to look for genetic susceptibility markers because maybe there's something in their actual genetic, in the patient's actual genetic makeup that.

00:13:36 Reid Oldenburg

results in them developing Ryme.

00:13:39 Reid Oldenburg

Maybe, for example, when they encounter a certain pathogen, like mycoplasma pneumonia is a very common trigger for Ryme.

00:13:45 Reid Oldenburg

Maybe when they encounter that, there's something in their genetic makeup, whether it be something like a cytokine or a protein recognition molecule that causes them to develop these things.

00:13:56 Reid Oldenburg

So I'm very looking forward to, they have a large team of collaborators that I can't name them all, but they have folks that are doing their informatics.

00:14:04 Reid Oldenburg

And I'm looking forward to understanding to see if, is there a genetic marker that can help us predict Ryme?

00:14:10 Reid Oldenburg

But I think also it's going to be really interesting to put these genetic markers into the context of inflammation and understand, you know, maybe it's going to help us really understand what inflammatory pathways are dysregulating in these patients as well.

00:14:22 Reid Oldenburg

So that's a really fun project that I'm looking forward to seeing results for.

00:14:26 Reid Oldenburg

We also have a lot of other clinical research projects.

00:14:29 Reid Oldenburg

So

00:14:30 Reid Oldenburg

Harper Price is doing work on survey work and just getting, once again, bringing our FSG talent together and understanding what some of the barriers, diagnostic needs are, treatment and management needs are for pediatric Stephen Johnson's or toxic epidermal necrolysis.

00:14:48 Reid Oldenburg

So SGS and TEN, for those of our listeners that are not as familiar with these terms, these are drug-triggered severe cutaneous adverse reactions that do resemble

00:15:00 Reid Oldenburg

rhyme.

00:15:01 Reid Oldenburg

And so the drug-triggered ones will cause blistering of the mucous membranes and the skin and can be very life-threatening and very scary, and they're triggered by medications.

00:15:11 Reid Oldenburg

But what's really important for us to evaluate from a clinical perspective, especially in pediatric patients, is how are providers using different therapies to treat the immune system?

00:15:23 Reid Oldenburg

And then how are we doing the basics, like wound care?

00:15:26 Reid Oldenburg

And

00:15:27 Reid Oldenburg

of the room temperature.

00:15:28 Reid Oldenburg

How are we actually, so really these minor details, because really the importance is really in this detailed multidisciplinary care.

00:15:34 Reid Oldenburg

So Harper Price is going to bring together some ideas from all over our community to really understand how these differences exist in different centers so that we can learn from each other.

00:15:45 Reid Oldenburg

So that's another really interesting clinical project.

00:15:50 Reid Oldenburg

I definitely also want to highlight the work from Fiona Lynch, who is one of our liaisons

00:15:56 Reid Oldenburg

who we're hoping to bring into the leadership of this FSG in the future, if she's able to, because she may be recruited somewhere else.

00:16:03 Reid Oldenburg

But if she's able to, we would love to recruit her.

00:16:05 Reid Oldenburg

And she's done a lot of work in terms of community engagement.

00:16:10 Reid Oldenburg

So, you know, reactive infectious mucocutaneous eruptions,

00:16:14 Reid Oldenburg

They're essentially, these pathogen triggered.

00:16:17 Reid Oldenburg

So people get walking pneumonia.

00:16:18 Reid Oldenburg

And then about a week later, they develop these horrible blisters of their mouth and eyes and can get hospitalized for, you know, for weeks at a time because they're unable to even eat.

00:16:28 Reid Oldenburg

And this affects, you know, children and it can happen over and over again.

00:16:32 Reid Oldenburg

So some patients will get it, you know, once a year or multiple times.

00:16:35 Reid Oldenburg

And it's extremely disruptive for patients.

00:16:38 Reid Oldenburg

they lose a lot of weight, they can't do sports, and it's a terrible disease.

00:16:41 Reid Oldenburg

So one thing that Fiona is doing is she's working to develop patient-centered resources.

00:16:47 Reid Oldenburg

So how do we have a patient-centered resource?

00:16:52 Reid Oldenburg

You know, how do we describe what rhyme is for folks that are affected by rhyme?

00:16:56 Reid Oldenburg

How do we put it into terminology that is easy to understand for, you know, a lot of our patients are 12, 13, 14 years old.

00:17:03 Reid Oldenburg

So

00:17:04 Reid Oldenburg

We're going to work, and Fiona's doing some excellent work to understand, different ways of conveying information to different age groups.

00:17:12 Reid Oldenburg

So I'm looking forward to see some of those patient-facing resources because we currently have a lack of those.

00:17:19 Reid Oldenburg

She's also coordinating with Yvonne Chu and Michelle Romine to help find patients for the genetic study.

00:17:25 Reid Oldenburg

And then she is doing retrospective studies, which basically means look at all the patients that had rhyme at

00:17:32 Reid Oldenburg

a center and then look back at how they did, what were the triggers, what was the treatment that was used, how did the patients actually do?

00:17:40 Reid Oldenburg

So she's putting together a really nice study looking back through records at her hospital and I'm looking forward to seeing a publication from her soon.

00:17:49 Reid Oldenburg

She has the manuscript is currently in writing there.

00:17:53 Reid Oldenburg

So I think, you know, she's been such a fun member of our group that's been very dynamic, so we're lucky to have her input as well.

00:18:01 Reid Oldenburg

And then

00:18:01 Reid Oldenburg

We're also, another thing we're doing is we're coordinating with another, and this is one thing that we're always trying to do is talk to our, how do we talk to our FSG colleagues, you know, because we have all these other FSG, and there's a lot of overlapping interests.

00:18:14 Reid Oldenburg

And one of the recent overlapping interests that we have is JAK inhibitors are now, of course, these are systemic small molecule inhibitors that are being used to

00:18:24 Reid Oldenburg

inhibit inflammation that is, and these medications are really helping patients who have atopic dermatitis or really bad eczema, and it's also helping one of our non-scarring hair loss disorders, alopecia areata.

00:18:36 Reid Oldenburg

So a lot of different patients in varying age groups are now on JAK inhibitors.

00:18:41 Reid Oldenburg

And we're working with an ongoing study to understand and see if JAK inhibitors are affecting certain patient outcomes, particularly their growth and how they're doing overall.

00:18:52 Reid Oldenburg

Because of course, JAK inhibitors are a newer medication.

00:18:55 Reid Oldenburg

And so we're doing a lot of work with others to improve the pharmacovigilance of these medications.

00:19:02 Jenn Dawson

Oh my gosh, that is a lot happening in this focus study group.

00:19:06 Jenn Dawson

I am thrilled to see so much wonderful work coming together, especially

00:19:11 Jenn Dawson

that piece about developing content that's appropriate for different age levels of patients.

00:19:17 Jenn Dawson

That is so important.

00:19:19 Jenn Dawson

So that's a pretty comprehensive overview of what the group is doing.

00:19:22 Jenn Dawson

And if it's okay with you, I just want to pause here on the research portion because some information just finally gelled for me about the work that Drugs and Bugs is actually doing.

00:19:32 Jenn Dawson

And I just want to go off on a little bit of a tangent here.

00:19:36 Jenn Dawson

So bear with me and listeners, I promise it'll be worth it.

00:19:39 Jenn Dawson

Way back almost three years ago in 2023, I recorded a podcast with Dr.

00:19:46 Jenn Dawson

Michelle Ramin, Dr.

00:19:47 Jenn Dawson

Erin Mathis, and Dr.

00:19:48 Jenn Dawson

Yvonne Chu, where we were really talking about the differences between rhyme, SJS, and TEN, and really kind of why the naming of these

00:20:02 Jenn Dawson

conditions matters.

00:20:04 Jenn Dawson

And you really helped crystallize for me that, rhyme is triggered by a pathogen where SJSTEN is triggered by medication or a treatment.

00:20:14 Jenn Dawson

That's not something that I think was really clear in my head, but now it is.

00:20:19 Jenn Dawson

So I want to talk to you a little bit about like how have we evolved since just 2023 when we were talking about this sort of being a jumbled up mess and why is

00:20:32 Jenn Dawson

is it important to have these specific definitions for these conditions?

00:20:37 Reid Oldenburg

Oh yeah, completely.

00:20:38 Reid Oldenburg

And I think this is where, the naming of diseases and identifying things is so important.

00:20:44 Reid Oldenburg

And if I was this discussion in medicine about lumpers and splitters, the reason, I think that the philosophical reason for splitting and for actually breaking down these diagnoses is because if the trigger, if the cause is different, then the actual

00:21:02 Reid Oldenburg

the actual inflammation and the actual problem that the patient is facing could be also different.

00:21:07 Reid Oldenburg

So just because things look similar does not actually mean that the trigger is the same exact thing.

00:21:14 Reid Oldenburg

And so it's actually pretty interesting because some patients with really bad, when they have really bad flares of lupus,

00:21:20 Reid Oldenburg

their reaction can actually have some overlapping features with what we see in Rime or SGS and TN.

00:21:28 Reid Oldenburg

So I really do think that, of course, you know, you do have to be careful with creating all these different names because you don't want to confuse the audience and you don't want to confuse, you know, you don't want to confuse people who may not see these diagnoses frequently.

00:21:40 Reid Oldenburg

I agree with the work done by other FSG members in that you really want to understand

00:21:47 Reid Oldenburg

what is the trigger so that we can actually direct a workup to properly diagnose the patients.

00:21:52 Reid Oldenburg

And then you do want to be able to have a clear diagnosis of pathogen triggered versus drug triggered because now we're starting to see that the pathogen triggered or RIME cases, the RIME cases actually have a different clinical course.

00:22:06 Reid Oldenburg

They tend to have less skin involvement.

00:22:10 Reid Oldenburg

they tend to more be younger and have more eye involvement.

00:22:14 Reid Oldenburg

And then they also, you want to have the appropriate diagnosis and understand rhyme because then you're going to look for that pathogen trigger, which in the case of mycoplasma, you can.

00:22:23 Reid Oldenburg

direct antimicrobial therapy to treat that.

00:22:26 Reid Oldenburg

And a lot of patients, will have actual, they'll have chest x-ray findings or they do have signs of atypical pneumonia.

00:22:32 Reid Oldenburg

So I really do agree with the work done by former, you know, by former really important publications about actually splitting this.

00:22:40 Reid Oldenburg

And I think this is where we're lucky to have a community like PeDRA because by bringing our resources together, we're able to have publications with consensus that means that these diagnostic terms will actually get

00:22:53 Reid Oldenburg

out of North America and we'll get to the rest of the world.

00:22:55 Reid Oldenburg

Because when you explain pathogen triggered, rhyme to people in other countries, they may not know that term.

00:23:02 Reid Oldenburg

So sometimes you actually have to say pathogen triggered SGSTN.

00:23:05 Reid Oldenburg

And so your confusion around the idea, and it's actually very, it's not even really a confusion.

00:23:12 Reid Oldenburg

It's more just we don't have consistency, you know, internationally in terms of

00:23:17 Reid Oldenburg

of what the nomenclature really is.

00:23:19 Reid Oldenburg

And so I think, just by repeating these publications, it's really valuable.

00:23:23 Reid Oldenburg

But I think even just putting a name rhyme on this, it was so valuable because it allows, funding agencies like the NIH and it allows for more directed research to understand some of these questions.

00:23:37 Reid Oldenburg

And so the mechanism that why does mycoplasma pneumonia, why does it cause mucocutaneous eruptions?

00:23:43 Reid Oldenburg

The mechanism has been

00:23:46 Reid Oldenburg

unknown.

00:23:46 Reid Oldenburg

And the first cases of this have been described over 100 years ago.

00:23:50 Reid Oldenburg

So it just really goes to show that when you name something and you start to split it and really have a clear diagnostic term, it really helps.

00:24:00 Reid Oldenburg

And of course, the obvious thing is that when you have a clear diagnostic term, it allows you to study

00:24:07 Reid Oldenburg

individualized and molecular based therapies for that specific thing.

00:24:12 Reid Oldenburg

Because as a patient, you don't want to be the one-size-fits-all.

00:24:15 Reid Oldenburg

Everyone is special and you want the treatment that works for you.

00:24:18 Reid Oldenburg

So of course, by having more individualized diagnostic and more precision in our diagnosis, it allows you to have a more precise treatment as well.

00:24:27 Jenn Dawson

That was so helpful.

00:24:29 Jenn Dawson

Thank you for allowing me that tangent.

00:24:33 Jenn Dawson

But it really illustrates why this work is so important.

00:24:36 Jenn Dawson

So let's use this time to shift into our conversation about some of the projects that you yourself are specifically working on.

00:24:43 Jenn Dawson

So I know you and several others all worked together on a recent publication that appeared in JCI Insight back in November that was supported by a 2020 PDA research grant.

00:24:56 Jenn Dawson

And the title of that project was Dual Dysregulation of TNF-IFN,

00:25:01 Jenn Dawson

signaling, and classical monocytes are implicated in reactive infectious mucocutaneous eruptions.

00:25:09 Jenn Dawson

And then you also published an abstract at the PDRA 2024 conference titled Deciphering the Immunopathogenesis of Reactive Infectious Mucocutaneous Euption.

00:25:22 Jenn Dawson

So talk a little bit more about those projects, possibly how they're linked, and what you're learning.

00:25:28 Reid Oldenburg

Right, and the thanks for, thanks for offering the opportunity to talk about this research, because of course it's very exciting and I think it's a really exciting time and it's really a good continuation on this idea of now that we have this diagnostic term, how do we, how can we break it apart and how can we actually understand the path of mechanisms of what is actually happening in these patients?

00:25:49 Reid Oldenburg

And the two projects are really linked because they're really just one long continuous journey.

00:25:56 Reid Oldenburg

And as our research listeners know, it's such a journey.

00:25:59 Reid Oldenburg

These projects always take longer.

00:26:02 Reid Oldenburg

Yeah, and essentially it's collaborative in a sense where we have been working collectively with our entire pediatric dermatology faculty here at Rady Children's Hospital, and we've been working with all the residents and have been working with two different basic science labs

00:26:19 Reid Oldenburg

and have also worked with collaborators that do bioinformatics at the La Jolla Institute for Immunology.

00:26:26 Reid Oldenburg

So we have a pretty large group of people.

00:26:28 Reid Oldenburg

And essentially what we're doing is we're collecting samples from active Rime patients.

00:26:34 Reid Oldenburg

So when they actually are experiencing the inflammatory effects of Rime, and we are taking their samples, we're taking their blood, and when we can, if it's possible, we get blister fluid from the patients.

00:26:47 Reid Oldenburg

And then what we do is we

00:26:49 Reid Oldenburg

we do what we call single cell RNA sequencing, which essentially means we take each individual cell from their blood or from their blister fluid, and we put them into little microchips essentially, and then we sequence all of the RNA, meaning the gene signature in each individual cell.

00:27:07 Reid Oldenburg

And even with like 10,000 or 15,000 cells, you can get an unbelievable amount of information because now what you're doing is you're looking at

00:27:17 Reid Oldenburg

not just all immune cells.

00:27:19 Reid Oldenburg

You're looking at the monocytes, the T cells, the B cells.

00:27:22 Reid Oldenburg

And then you can see what inflammatory pathways are upregulated in the patients.

00:27:28 Reid Oldenburg

And it's very difficult research.

00:27:29 Reid Oldenburg

So essentially, the biggest challenge is actually getting the patients, finding the patients in the emergency department early on.

00:27:37 Reid Oldenburg

and then also finding them when they've recovered.

00:27:40 Reid Oldenburg

Because what we do is we get their sample while they're having active Ryme, and then we find them, usually three months, six months later, and then we ask them for another sample so that we can compare their inflammation to when they're recovered.

00:27:55 Reid Oldenburg

And this has been really valuable.

00:27:57 Reid Oldenburg

And our first, you know, our first publication

00:28:00 Reid Oldenburg

on this was a group of all comers with Ryme.

00:28:04 Reid Oldenburg

So we found any patient that had Ryme, and then what we did is we took their serum and we sent it for cytokine analysis, and we looked at almost, I think it was 300 different cytokines.

00:28:14 Reid Oldenburg

and we identified to see if there was an overlapping, inflammatory signature.

00:28:20 Reid Oldenburg

So like, you have five different RIME patients.

00:28:22 Reid Oldenburg

Are they similar?

00:28:23 Reid Oldenburg

Do they have the same inflammatory signaling?

00:28:25 Reid Oldenburg

Because maybe they have different triggers.

00:28:27 Reid Oldenburg

Maybe one had, you know, COVID was a trigger, one had adenovirus as a trigger, another one had mycoplasma.

00:28:32 Reid Oldenburg

And it's really interesting to actually look at this diverse group of patients with different triggers and see if there's actual overlapping inflammatory signaling.

00:28:42 Reid Oldenburg

And this first initial report that we published

00:28:44 Reid Oldenburg

published, I think it was just two months ago now, was able to identify that there is a signature that we think links dysregulation of TNF, which is an important cytokine, and then also interferon signatures.

00:29:01 Reid Oldenburg

So the TNF piece is very validating and important because currently one of the

00:29:09 Reid Oldenburg

more accepted therapies for Ryme is a tannerceptor, which actually inhibits TNF-alpha.

00:29:17 Reid Oldenburg

So that TNF is an inflammatory cytokine.

00:29:21 Reid Oldenburg

And we know, extrapolating from the literature from SGS and TN from the drug-induced ones, we know that TNF is probably contributing to cell death, which is the, you know, of course, the mucous membranes and the skin.

00:29:32 Reid Oldenburg

And so we were able to validate that in this small series that there's dysregulation in these two things.

00:29:39 Reid Oldenburg

It's definitely a nice step, but I really think we have a ton more work to do.

00:29:44 Reid Oldenburg

the upcoming project now that we're doing is we've been collecting samples just of patients with mycoplasma pneumonia-triggered RIME.

00:29:53 Reid Oldenburg

And the reason why we want to do that is because we really want to try and collect a very consolidated group of patients so that we can

00:30:01 Reid Oldenburg

we can further dig and do more of the transcriptomics.

00:30:04 Reid Oldenburg

And so I'm very happy that PeDRA actually is supporting the next phase of this research.

00:30:11 Reid Oldenburg

So I'm very lucky.

00:30:11 Reid Oldenburg

And I just want to thank PeDRA, of course, for funding the next grant, which will actually continue to do this work in these patient samples.

00:30:21 Reid Oldenburg

Because now, of course, it's been four or five years since I've been collecting these samples.

00:30:24 Reid Oldenburg

So now we have more samples that we can analyze.

00:30:27 Jenn Dawson

I'm wondering if you could comment or talk a little bit about the value of bringing in other specialties when you're working on projects like this.

00:30:35 Jenn Dawson

Like you mentioned, you're working with people in immunology.

00:30:38 Jenn Dawson

I see that Bob Gang is on your publication.

00:30:43 Jenn Dawson

So why is it important to bring other specialties to the table?

00:30:49 Reid Oldenburg

It's the potential of working

00:30:52 Reid Oldenburg

interdisciplinary is really endless.

00:30:54 Reid Oldenburg

And I think it comes from a lot of different angles.

00:30:56 Reid Oldenburg

I mean, first of all, bringing people from other specialties is valuable because they have had similar questions in their field.

00:31:04 Reid Oldenburg

So a good example is Hal Hoffman, who worked a lot with the periodic fever syndromes.

00:31:09 Reid Oldenburg

There were so many questions that he had to answer.

00:31:11 Reid Oldenburg

And so just talking to someone like him

00:31:14 Reid Oldenburg

or talking to someone, one of the Kawasaki disease experts and just saying, how did you start your work?

00:31:19 Reid Oldenburg

How did you break this down?

00:31:21 Reid Oldenburg

So there's just almost, you know, it's almost like an apprenticeship.

00:31:23 Reid Oldenburg

It's just asking, it's just asking people, well, how did you do it?

00:31:27 Reid Oldenburg

And I think just through experience, through learning from others, and then, you know, rheumatology, for example, they have all these inflammatory markers.

00:31:34 Reid Oldenburg

Bob Gang works in allergy and immunology.

00:31:37 Reid Oldenburg

So there's this whole other experience in, you know,

00:31:42 Reid Oldenburg

genes, inflammation, understanding rare diseases that comes from that.

00:31:47 Reid Oldenburg

So essentially by bringing together a large group of mentors and colleagues or whatever you want to call them, I'm able to get experience and learn from them directly from a pragmatic standpoint.

00:31:58 Reid Oldenburg

So how did you do this?

00:31:59 Reid Oldenburg

Oh, I did it this way.

00:32:01 Reid Oldenburg

You know, having an IRB, you talk to the IRB.

00:32:04 Reid Oldenburg

Then of course, you know, when it comes to some of the more nuts and bolts,

00:32:08 Reid Oldenburg

you mentioned collaboration.

00:32:09 Reid Oldenburg

So we have a key set of collaborators with bioinformatics.

00:32:13 Reid Oldenburg

And so obviously, I'm not capable of sitting and coding and doing all the codes.

00:32:20 Reid Oldenburg

So, the best thing that I can do is from my clinical perspective, I have this perspective that I can offer.

00:32:26 Reid Oldenburg

And the best thing that I'll do is I'll sit next to the bioinformatician and, you know, we'll just talk, you know, over the course of a day.

00:32:33 Reid Oldenburg

I'll look at the data and see what the inflammatory signaling is in real time, what the single cell RNA sequencing is showing.

00:32:41 Reid Oldenburg

And then when I look at the data, I'm able to, through experience and once again talking to this collaborative network, I'm able to pick out the inflammatory markers that have a story behind them and actually make sense in the context of the patient.

00:32:56 Reid Oldenburg

So the informatician is really

00:32:59 Reid Oldenburg

they're really able to dig deep, but then it comes to, then it comes to us and it comes to me in this meeting setting.

00:33:06 Reid Oldenburg

And then we're able to take everything in context and say, okay, well, what does this actually mean?

00:33:11 Reid Oldenburg

Does this mean that we can use a different therapy for this?

00:33:14 Reid Oldenburg

Can we analyze this?

00:33:15 Reid Oldenburg

Can we analyze that?

00:33:16 Reid Oldenburg

And it's really that back and forth that allows the work to go.

00:33:19 Reid Oldenburg

But I mean, to answer your question, I mean, it's really just, there's so much benefit that you get from working with people.

00:33:27 Reid Oldenburg

And having the right people that share the motivation is so critical.

00:33:31 Jenn Dawson

Yeah, I really like how you put it, especially when you said that their questions probably aren't so different from the questions you're asking too.

00:33:38 Jenn Dawson

And so you have this chance to really work together.

00:33:42 Jenn Dawson

And then everybody brings their box of puzzle pieces.

00:33:45 Jenn Dawson

And then with everybody there, you can start putting the puzzle together.

00:33:50 Reid Oldenburg

Yeah, absolutely.

00:33:50 Reid Oldenburg

and I definitely actually want to also give a shout out to Lori Broderick, who helped me contextualize things and understand inflammation and really break things down because she had a fantastic story looking at pansquotic morfare.

00:34:04 Reid Oldenburg

And it was very similar.

00:34:05 Reid Oldenburg

It was, you know, these diseases have been understudied and how do you break apart these available tools and how do you apply it to a problem?

00:34:13 Reid Oldenburg

So, yeah, I mean, completely, it's all about it's all about that persistence, but it's all about, you know, working together and then also

00:34:20 Reid Oldenburg

So, just communicating clearly with team members and just taking that time to just have patience.

00:34:27 Reid Oldenburg

everyone has a different skill set, so sometimes we almost need like a translator there to talk to each other, but we get through it, and it's really just the patience and the communication that brings everything together.

00:34:38 Jenn Dawson

Yeah, it sounds like just a really impressive group that you all have assembled and have going.

00:34:44 Jenn Dawson

And I know that your efforts will be rewarded, certainly.

00:34:48 Jenn Dawson

We are coming to the end of our interview, which I am not happy about because I feel like there's so much more we could talk about.

00:34:56 Jenn Dawson

But I just wanted to close with a few final questions.

00:35:02 Jenn Dawson

I want to think about the future.

00:35:05 Jenn Dawson

I want to think about the future of the Drugs and Bugs Group and of your career and your inspiration and your work in research and where you see all of that in the next five years.

00:35:20 Reid Oldenburg

Right, yeah, thanks for the question.

00:35:21 Reid Oldenburg

It's been such a fun discussion too so far.

00:35:23 Reid Oldenburg

You know, I think what will be really valuable for the FSG is really just continuing a lot of these projects.

00:35:30 Reid Oldenburg

And I think,

00:35:32 Reid Oldenburg

And I think we need to, with, and I won't be, I think next year I won't be president.

00:35:36 Reid Oldenburg

So I think the next leadership, we're really going to have to continue to work to bring in other topics outside of Rhyme, because we've really been focused on Rhyme and SGS.

00:35:46 Reid Oldenburg

And then also, I didn't really mention DRESS syndrome, but I think there's a lot of opportunities in the world of DRESS syndrome.

00:35:51 Reid Oldenburg

So I think, you know, the first thing we want to do is we want to continue the clinical work.

00:35:56 Reid Oldenburg

We want to build more consensus.

00:35:58 Reid Oldenburg

And then another thing that I think in Rhyme that we have in our early phases, and we're talking to different members, is we're going to need to develop an activity score.

00:36:09 Reid Oldenburg

Because for Rhyme, it's really hard to tell, and our expert clinicians certainly can, and we know they can, but it's very hard to tell for people with lower patient volume or residents, it's really hard to tell how active

00:36:22 Reid Oldenburg

the patient actually is like, are they getting worse?

00:36:24 Reid Oldenburg

Is there inflammation?

00:36:26 Reid Oldenburg

How do we know that a treatment is not working?

00:36:29 Reid Oldenburg

And so one thing I'm currently in early discussion with Yvonne Chu and Michelle Ramin is we're going to try and develop a clinical activity score for RIME.

00:36:38 Reid Oldenburg

And I think an activity score will be really good because it's different from severity because activity is going to really help us in real time understand what's happening with the patient.

00:36:47 Reid Oldenburg

How do we

00:36:48 Reid Oldenburg

How do we proceed with treatment?

00:36:49 Reid Oldenburg

So that's one thing I think is going to be valuable from the clinical perspective is an activity score.

00:36:54 Reid Oldenburg

And severity score is also important as well.

00:36:56 Reid Oldenburg

RIME does not have an ICD-10 code.

00:36:58 Reid Oldenburg

So that's another thing that we should be working on the next once to years.

00:37:02 Reid Oldenburg

There's no ICD-10 code for RIME.

00:37:04 Reid Oldenburg

And it's very hard to even identify cases.

00:37:06 Reid Oldenburg

And as you know, you've talked to a lot of different clinical researchers that if you don't have good data, it's hard to actually get a good message.

00:37:13 Reid Oldenburg

So I think we need to do a better job of

00:37:16 Reid Oldenburg

talking to the coders and engage with the responsible bodies like the CDC and actually have an ICD-10 code.

00:37:23 Reid Oldenburg

So these are some of the short-term things.

00:37:24 Reid Oldenburg

I mentioned the consensus guidelines and I think every one to two to three years we should probably be updating these consensus guidelines because RIME is a very actively moving field.

00:37:36 Reid Oldenburg

So in that sense, you know, I think that's going to be probably the mid-term goals for PeDRA is really continuing some of this work.

00:37:43 Reid Oldenburg

Of course, the basic science.

00:37:44 Reid Oldenburg

Thanks for giving me a chance to talk about some of

00:37:46 Reid Oldenburg

the basic science work.

00:37:47 Reid Oldenburg

I think the basic science work also in the midterm will be critical to continue.

00:37:52 Reid Oldenburg

And I think applying for larger funds from the NIH will really help answer some of these more mechanistic questions.

00:37:59 Reid Oldenburg

The third thing is I think we need to do more in

00:38:04 Reid Oldenburg

understanding and doing group collective efforts to look back and see what's happening in the drug-induced SGS and TN.

00:38:12 Reid Oldenburg

So Stephen Johnson's in toxic epidermal necrolysis.

00:38:15 Reid Oldenburg

And I think we need to do a better job of

00:38:17 Reid Oldenburg

of really looking at pediatric dermatology cases and looking retrospectively at outcomes and usage of different medications, because now there's some new data in the adult literature, and it's a little bit complicated because some of those patients were on immunomodulatory therapies for cancer therapy, but there's new data to suggest that JAK inhibitors may be very valuable for S-Jacintin.

00:38:41 Reid Oldenburg

And I think we need to start to

00:38:44 Reid Oldenburg

me to start to approach some of these questions that have been partially answered in the adult population and work to understand in pediatrics what, in our pediatric population, what is actually happening.

00:38:55 Reid Oldenburg

So I think that's a major question.

00:38:58 Reid Oldenburg

And then also, you know, just bringing in more ideas, bringing in our newer members, our younger faculty, our residents into the group to just bring more project ideas about medications in general.

00:39:10 Reid Oldenburg

You know, I think we have more work to do in

00:39:13 Reid Oldenburg

in urticarial dermatitis that may be triggered by medications, some of these other drug reactions.

00:39:21 Reid Oldenburg

And there's definitely a lot of opportunities.

00:39:23 Reid Oldenburg

So we definitely invite people to come to our sessions and engage with us online as well so that we can start to put our heads together to answer more things.

00:39:32 Reid Oldenburg

But yeah, good question.

00:39:35 Reid Oldenburg

More work is ongoing and more results to come, but we certainly have more work to do.

00:39:39 Reid Oldenburg

I don't think it's, I don't think it's ever gonna end.

00:39:42 Reid Oldenburg

I think we have so much things to look into.

00:39:45 Jenn Dawson

I think maybe I'll stop asking the futures question because it always is more work, more things that we need to do.

00:39:53 Jenn Dawson

We have more questions that need answering.

00:39:56 Jenn Dawson

But I think that the goals that you outlined there are really tremendous and highly achievable.

00:40:01 Jenn Dawson

And I'm so thankful that you are in the network and thinking about these things and getting others to think about them as well.

00:40:08 Jenn Dawson

One thing that I'm just personally curious about when it comes to you is, has there ever been

00:40:15 Jenn Dawson

like a publication or a study that you've come across that just totally flipped your thinking on something.

00:40:23 Reid Oldenburg

Yeah, and I think this really links up to some of the conversations, and it's not going to surprise you a lot of ways.

00:40:28 Reid Oldenburg

But in 2020, there was a paper where there was a patient that had a different severe cutaneous adverse reaction that we don't really cover in this discussion today called DRESS syndrome.

00:40:37 Reid Oldenburg

And that patient

00:40:39 Reid Oldenburg

was failing multiple therapies and had a very prolonged course and was on long-term systemic corticosteroids like prednisone.

00:40:46 Reid Oldenburg

And long-term prednisone, as many of our listeners know, it's not good for the body.

00:40:51 Reid Oldenburg

It causes metabolic dysfunction.

00:40:53 Reid Oldenburg

It's not good for bone density.

00:40:55 Reid Oldenburg

It has increased risks of infection.

00:40:57 Reid Oldenburg

So this patient was really suffering A lot.

00:40:59 Reid Oldenburg

And they did essentially, you know, what I've been talking about and what really excites me is they did some of these transcriptomics approaches and they identified the

00:41:09 Reid Oldenburg

inflammatory signature that was dysregulated in the patient.

00:41:13 Reid Oldenburg

And they ended up using an ex vivo preparation, meaning that they took the patient's cell out, they put it in a Petri dish, and then they treated it with a drug, and the drug worked in the Petri dish.

00:41:22 Reid Oldenburg

And then they actually, since the drug was FDA approved, they were able to use it off-label, of course, with extensive, this was at the NIH, by the way.

00:41:29 Reid Oldenburg

So of course, with extensive, you know, discussion with the patient and making sure everything ethically was okay, and they were using FDA approved dosing,

00:41:36 Reid Oldenburg

they were able to make the patient better using one of those small molecule JAK inhibitors.

00:41:40 Reid Oldenburg

And so that's just, to me, that's just like very mind-boggling.

00:41:43 Reid Oldenburg

And that happened in 2020.

00:41:45 Reid Oldenburg

And I think it was just like, it really was that sort of evidence of, you know, you can actually using these somewhat, that seem somewhat esoteric techniques, you can actually immediately turn around and help a patient.

00:41:59 Reid Oldenburg

So that was probably, that was the first thing that came to my mind when you said that.

00:42:02 Reid Oldenburg

But there's so many studies that are landmark and

00:42:06 Reid Oldenburg

groundbreaking as well.

00:42:08 Jenn Dawson

Well, thank you for letting me put you on the spot with that question.

00:42:11 Jenn Dawson

And I'm wondering for our listeners who are less familiar, if you could just give a quick description of dress syndrome.

00:42:18 Reid Oldenburg

Right, so DRESS syndrome is drug reaction with eosinophilia and systemic symptoms.

00:42:23 Reid Oldenburg

And this is another drug reaction.

00:42:25 Reid Oldenburg

So typically, you know, common things that cause DRESS syndrome would be an antibiotic and so, or an anti-epileptic, something that people are taking for seizures.

00:42:36 Reid Oldenburg

So after a few weeks, usually somewhere in the range of two to six, maybe 8 weeks, patients with dress develop organ damage in a rash.

00:42:45 Reid Oldenburg

So they get red, they get swelling of their head and neck.

00:42:49 Reid Oldenburg

And then in a lot of patients, they develop some type of organ damage.

00:42:53 Reid Oldenburg

Usually it's the liver or the kidneys.

00:42:55 Reid Oldenburg

And it's very scary.

00:42:56 Reid Oldenburg

And about 5 to 10%, but let's say 5% of patients, it actually can be fatal.

00:43:01 Reid Oldenburg

So it's really a scary thing in dermatology.

00:43:03 Reid Oldenburg

And we treat it by, of course, withdrawing the medication that caused it and then putting it on an adverse reaction list.

00:43:11 Reid Oldenburg

So never take it again.

00:43:12 Reid Oldenburg

Some of the patients get a bracelet.

00:43:13 Reid Oldenburg

Don't ever take it again, just like SGS and TM.

00:43:16 Reid Oldenburg

Don't take that medication again.

00:43:17 Reid Oldenburg

And then we treat it with immunomodulatory therapy, with the most common one being prednisone.

00:43:22 Reid Oldenburg

And the patients, they get, interestingly enough, they get very high eosinophil counts.

00:43:26 Reid Oldenburg

And we know that eosinophils are somewhat important because

00:43:31 Reid Oldenburg

if a biopsy is done in the skin or an organ like the heart or the liver, they can see eosinophils there as well.

00:43:37 Reid Oldenburg

And we know that also lymphocytes such as T-cells are really important as well.

00:43:41 Reid Oldenburg

And so the combination of this reaction with the medication and elevated T-cells in the blood and in the tissue is causing skin, but also organ damage.

00:43:52 Reid Oldenburg

So it's a really scary disease in dermatology and it's another severe cutaneous adverse reaction.

00:43:56 Jenn Dawson

The human body and our immune system never ceases to amaze me.

00:44:01 Reid Oldenburg

I mean, it's really amazing how our immune system has evolved to really, you know, prevent us from getting infection, but also the immune system is also preventing us from getting cancer.

00:44:11 Reid Oldenburg

You know, I heard recently that our immune system is maybe getting rid of 1 cancer a day in our body.

00:44:15 Reid Oldenburg

And I think it's,

00:44:17 Reid Oldenburg

It's really, it's not just the immune system, it's not just doing infections.

00:44:20 Reid Oldenburg

So it's really amazing that our immune system is able in so many situations to not go completely haywire and cause a lot of inflammation.

00:44:28 Reid Oldenburg

And of course, you know, the diseases in dermatology that we need to do better on is really understand how the inflammation

00:44:34 Reid Oldenburg

this dysregulated inflammation that's supposed to do the right thing is not working for us in certain disease states.

00:44:40 Reid Oldenburg

And I think that's where it's really, immunology is so fascinating in that way where you know that we need our immune system, but sometimes it can do the wrong thing, unfortunately.

00:44:49 Jenn Dawson

Yeah, sometimes our immune systems just get carried away.

00:44:53 Jenn Dawson

So thank goodness you and your colleagues are putting in so much time and effort to study this.

00:44:59 Jenn Dawson

thank you so much for joining me on Pedro Pearls today, Dr.

00:45:03 Jenn Dawson

Oldenburg.

00:45:04 Jenn Dawson

It's always a pleasure talking with you.

00:45:06 Jenn Dawson

I always learn so much.

00:45:07 Jenn Dawson

I hope others in the network and those who are listening feel the same way.

00:45:11 Jenn Dawson

Thank you so much for joining me.

00:45:14 Reid Oldenburg

Thank you so much.

00:45:15 Reid Oldenburg

Yeah, it was so fun to discuss with you and thanks for bringing such a fun discussion.

00:45:19 Reid Oldenburg

I really appreciate it.

00:45:25 Jenn Dawson

I'd like to take a moment to thank PeDRA's corporate council members.

00:45:29 Jenn Dawson

Our gold-level supporters are Eli Lilly and Sanofi and Regeneron Pharmaceuticals.

00:45:34 Jenn Dawson

Our silver-level supporters are AbbVie, Abeona Therapeutics, Arcutis Biotherapeutics, Chiesi, Incyte, Sanofi, and UCB.

00:45:46 Jenn Dawson

And our bronze-level supporters are DISC Medicine, Janssen, and Pfizer.

00:45:51 Jenn Dawson

We so appreciate their shared commitment to PeDRA's mission as members of the PeDRA Corporate Council.

00:45:58 Jenn Dawson

Thanks so much for listening to PeDRA Pearls.

00:46:00 Jenn Dawson

If you enjoyed this episode, be sure to follow us or subscribe to the PeDRA Pearls Podcast channel wherever you listen so you don't miss future conversations.

00:46:10 Jenn Dawson

To learn more about PeDRA and our work to advance research in pediatric dermatology, visit PeDRAresearch.org or follow us on social media @PeDRAResearch.

00:46:23 Jenn Dawson

Until next time, keep listening, learning, and collaborating to make a difference for kids with skin disease.